Indian Pacing and Electrophysiology Journal (Sep 2013)

Quinidine: an “Endangered Species” Drug Appropriate for Management of Electrical Storm in Brugada Syndrome

  • Stelios Paraskevaidis, MD, PhD,
  • Efstratios K. Theofilogiannakos, MD, PhD,
  • Vasileios Kamperidis, MD,
  • Yiannis S. Chatzizisis, MD, PhD,
  • Konstantinos Tsilonis, MD,
  • Vassilios P. Vassilikos, MD, PhD,
  • George Dakos, MD, PhD,
  • George Stavropoulos, MD,
  • Antonios Ziakas, MD, PhD,
  • Stavros Hadjimiltiades, MD, PhD,
  • Ioannis H. Styliadis, MD, PhD

DOI
https://doi.org/10.1016/S0972-6292(16)30670-2
Journal volume & issue
Vol. 13, no. 5
pp. 178 – 180

Abstract

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Brugada syndrome is an inherited channelopathy associated with an increased risk of syncope and sudden cardiac death. In rare cases it can be manifested with electrical storm. We report two cases of Brugada syndrome that presented with electrical storm and were treated successfully with oral quinidine, an "endangered species" drug.

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