A case of unusual renal manifestation in a patient with neuronal intranuclear inclusion disease treated with steroids

Abstract

Key Clinical Message Neuronal intranuclear inclusion disease (NIID) is a progressive neurodegenerative disorder characterized by intranuclear inclusions. Kidney injury involvement and successful treatment for NIID have rarely been reported. A NIID patient developed crescentic IgA nephropathy. Steroid therapy resolved digestive symptoms and recovered renal function. Steroids are considered for concomitant symptoms of NIID.

Keywords

• crescentic nephritis
• fibroblast
• IgA nephropathy
• neuronal intranuclear inclusion disease
• steroids