Lipomatous hemangiopericytoma of the larynx: An extremely rare tumor at an unusual location

Abstract

Hemangiopericytoma (HPC) arising from the contractile pericyte of Zimmerman comprises less than 1% of the vascular tumors with approximately 200 cases documented in the literature, out of which only 11 cases are reported in the larynx. Lipomatous hemangiopericytoma (LHPC) is an uncommon histological variant composed of a mixture of HPC and mature lipomatous component with around 50 cases reported so far, and majority have been found in the deep soft tissue of the lower extremities and retroperitoneum. HPCs are closely related to solitary fibrous tumors, and the LHPC was designated as a separate entity according to recent the World Health Organization classification of soft tissue tumors in 2002. To the best of our knowledge, even on extensive search of literature, LHPC of the larynx has not been reported till date. We report an extremely rare case of LHPC in a middle-aged female presented with a mass in the arytenoid cartilage of the larynx.

Keywords

• hemangiopericytoma
• larynx
• lipomatous hemangiopericytoma
• solitary fibrous tumor