A Variant of Gorlin–Goltz Syndrome with Synchronous Malignant and Multiple Benign Lesions of the Jaws - A Case Report

Abstract

Introduction: Although numerous syndromic and non-syndromic odontogenic lesions of the jaws have been documented in the literature, there are very few cases of simultaneous benign and malignant jaw lesions. Patient Concerns: We present a case of right maxillary squamous cell carcinoma along with several benign odontogenic cystic lesions of the jaws and skeletal abnormalities that meet the criteria for Gorlin-Goltz syndrome. Take-Away Lessons: With a review of the literature, the specifics of management and follow-up are discussed.

Keywords

• dentigerous cyst
• gorlin–goltz syndrome
• odontogenic keratocyst
• squamous cell carcinoma
• synchronous neoplasms