Journal of Tehran University Heart Center (Mar 2017)

Primary Cardiac Synovial Sarcoma: A Case Report

  • Mahmood Hosseinzadeh Maleki,
  • Moein Aboobakri Makouei,
  • Farbod Hatami,
  • Reza Zeinabadi Noghabi

Journal volume & issue
Vol. 12, no. 1

Abstract

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Primary cardiac sarcomas are rare clinical entities with an incidence rate of 0.0001% in collected autopsy series and are regarded as very aggressive tumors. We herein describe a 21-year-old woman presenting with syncope, dyspnea, and abdominal distention. She suffered from massive ascites, plural effusion, and liver congestion demonstrated by abdominal sonography and chest X-ray. Transthoracic echocardiography revealed a heterogeneous solid mass located in the right atrium; therefore, the patient underwent radical surgical excision of the tumor and 3 cycles of adjuvant chemotherapy. Fifteen months after surgery, she was having a favorable life quality without any evidence of recurrence.

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