Outcome and characteristics of nonsecretory multiple myeloma compared with secretory multiple myeloma: a retrospective multicenter study from China
Hailu Sun,
Aijun Liu,
Lihong Liu,
Wei Wang,
Zhen Cai,
Hua Yan,
Lijuan Chen,
Guangxun Gao,
Fang Wang,
Aijun Liao,
Bing Chen,
Jia Feng,
Juan Li,
Dong-Ping Huang,
Da Gao,
Qi-Ke Zhang,
Jun Luo,
Rong Fu,
Juan Du,
Jin Lu
Affiliations
Hailu Sun
Peking University People’s Hospital, Peking University Institute of Hematology, National Clinical Research Center for Hematologic Disease, Beijing Key Laboratory of Hematopoietic Stem Cell Transplantation
Aijun Liu
Department of Hematology, Beijing Chaoyang Hospital, Capital Medical University
Lihong Liu
Department of Hematology, The Fourth Hospital of Hebei Medical University
Wei Wang
Department of Hematology, The Affiliated Hospital of Qingdao University
Zhen Cai
Bone Marrow Transplantation Center, the First Affiliated Hospital, Zhejiang University School of Medicine
Hua Yan
Department of Hematology, Ruijin Hospital, Shanghai Jiaotong University School of Medicine
Lijuan Chen
Department of Hematology, Jiangsu Province Hospital, The First Affiliated Hospital With Nanjing Medical University
Guangxun Gao
Department of Hematology, Xijing Hospital, Air Force Medical University
Fang Wang
Department of Hematology, The First Affiliated Hospital of Zhengzhou University
Aijun Liao
Haematology Department of Shengjing Hospital, China Medical University
Bing Chen
Department of Hematology, The Affiliated Drum Tower Hospital of Nanjing University Medical School
Jia Feng
Department of Hematology, Peking University Shenzhen Hospital
Juan Li
Department of Hematology, The First Affiliated Hospital of Sun Yat-Sen University
Dong-Ping Huang
Department of Hematology, Yijishan Hospital, The First Affiliated Hospital of Wannan Medical College
Da Gao
Department of Hematology, the Affiliated Hospital of Inner Mongolia Medical University
Qi-Ke Zhang
Department of Hematology, People’s Hospital of Gansu Province
Jun Luo
The First Affiliated Hospital of Guangxi Medical University
Rong Fu
Department of Hematology, Tianjin Medical University General Hospital
Juan Du
Department of Hematology, Myeloma & Lymphoma Center, Shanghai Changzheng Hospital, Naval medical University
Jin Lu
Peking University People’s Hospital, Peking University Institute of Hematology, National Clinical Research Center for Hematologic Disease, Beijing Key Laboratory of Hematopoietic Stem Cell Transplantation
Abstract Background Nonsecretory multiple myeloma (NSMM) is a rare type of multiple myeloma (MM). Few studies have described the clinical features and outcomes of NSMM in novel agents. Additionally, the prognostic characteristics have remained controversial in recent years. Purpose To investigate the clinical and prognostic features of NSMM and explore the prognostic value of involved free light chain (FLC) levels in NSMM patients in the Chinese population. Methods We retrospectively enrolled 176 newly diagnosed NSMM cases between January 2005 and December 2021 from 19 clinical centers in China. The control group was selected using a 1:4 propensity score matching technique of newly diagnosed secretory MM, with age, sex and diagnosis time as the matching variables. Results The median age of NSMM patients was 60 years, and 22.6% of patients were classified as ISS stage 3. The ORR of the NSMM patients was 87.4%, and the CR was 65.8%. Compared to the matched secretory MM patients, more NSMM patients achieved CR after first-line treatment (65.8% vs. 36%, p = 0.000). The ORR of first-line treatment was not significantly different between NSMM and secretory MM (89.45% vs. 84.7%, p = 0.196). The first-line PFS was 27.5 m and 23 m (p = 0.063), and the median OS was 81 m and 70 months (p = 0.401). However, for CR-achieved NSMM and CR-not-achieved NSMM patients, the median PFS was 37 m vs. 16 m (p = 0.021), while the median OS showed no difference (107 m vs. 87 m, p = 0.290). In multivariate analysis, the significant factors for PFS were age ≥ 65 and ISS-3. ISS-3 was the only independent prognostic factor of OS. The iFLC ≥ 50 mg/L group had a high ORR of 97.3%, and the median PFS and OS were 48 m and NR, respectively. Compared to the matched secretory MM, the iFLC ≥ 50 mg/L group also showed more CR and longer OS (NR vs. 70 m, p = 0.006) and PFS (48 m vs. 23 m, p = 0.003). Conclusions Our results revealed that Chinese NSMM patients are younger and have a higher CR but not superior survival. The subgroup of NSMM patients with iFLC ≥ 50 mg/L had better outcomes than secretory MM.