Unilateral Pulmonary Aplasia with Dextroposition of Heart: A Case Report

Abstract

‘Pulmonary Aplasia’ is a rare condition where there is absence of unilateral or bilateral lung tissue with a rudimentary bronchus which separates it from the similar looking ‘Pulmonary Agenesis’. The aetiology is not completely understood, though a defect in chromosome number two is often associated. Failure of development of primary lung bud leads to aplasia/agenesis. It is often associated with other anomalies involving skeletal, cardiovascular, genitourinary and gastrointestinal system. We present a case of right sided pulmonary aplasia with dextroposition/levorotation of heart in a 10-month-old female child.

Keywords

• levorotation of heart
• lung herniation
• respiratory distress