FEJERMAN SYNDROME (BENIGN NONEPILEPTIC MYOCLONUS OF INFANCY)

Abstract

Abstract: Fejerman syndrome (benign nonepileptic myoclonus of infancy) is a rare nonepileptic paroxysmal disorder, characterized by typical presentation of short head nodding or shuddering in otherwise healthy infant without focal signs or psychomotor retardation and not associated with epileptiform abnormalities on EEG. Onset of this disorder occurs at first year of life (predominantly 6 months). Prognosis is benign with spontaneous disappearing of paroxysmal episodes by age of 2-3 years. This syndrome is poorly described in Russian literature. We present the description of our own clinical cases.

Keywords

• fejerman syndrome
• benign nonepileptic myoclonus of infancy
• epileptic spasms
• video-eeg monitoring