Radiology Case Reports (Aug 2024)

Minor's syndrome: Dehiscence of the superior semicircular canal. A case report

  • Hajar Zebbakh, MD,
  • Kenza Sidki, MD,
  • Fatima Zahra Laamrani, PhD,
  • Laila Jroundi, PhD,
  • Omar El Aoufir, PhD

Journal volume & issue
Vol. 19, no. 8
pp. 3321 – 3323

Abstract

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Superior semicircular canal (SSC) dehiscence syndrome, also known as Minor syndrome, is a rare condition characterized by vestibular and cochlear symptoms linked to a defect in the bony roof of the SSC. The prevalence is estimated at 0.5%, with a male predominance. Dehiscence may result from abnormal bone development, becoming symptomatic due to minimal trauma or pressure changes. Clinical presentation varies based on dehiscence size and location, with dizziness and oscillatory movements triggered by pressure changes or loud sounds being common symptoms. Other manifestations include conductive hearing loss due to the formation of a ``third window'' in the inner ear. Diagnosis typically involves computed tomography, distinguishing SSCDS from otosclerosis. Surgical treatment is reserved for cases of disabling vestibular pathology, often involving sealing the dehiscence through various approaches

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