Posterior Scleritis and Myelodisplasia in Relapsing Polychondritis- Case Report and Literature Review

Abstract

Relapsing Polychondritis (RP) is a rare, recurrent and autoimmune multisytem disorder affecting cartilaginous structures, such as: auricles, joints, nasal septum, larynx and tracheobronchial tree. Ocular manifestations may appear in 42,3-65% of cases (1,2), episcleritis and scleritis being the most common. However, it is often presented in an enigmatic fashion and is misdiagnosed, leading to potentially severe, debilitating and, sometimes, fatal disease. There is no established standardized therapeutic protocol for RP. Current medical therapy is largely empiric and based on case reports. The aim of this paper is to document one more case of ocular involvement in RP disease emphasizing the clinical and imaging findings that can help to establish an early diagnosis. Keywords: Relapsing Polychondritis; Autoimmune disease; Myelodysplastic Syndrome; Scleritis/treatment; Case Reports

Keywords

• Relapsing Polychondritis
• Autoimmune disease
• Myelodysplastic Syndrome
• Scleritis/treatment
• Case Reports