Arrhythmogenic right ventricular cardiomyopathy: A case report and review of literature

Abstract

Arrhythmogenicright ventricular cardiomyopathy (also called arrhythmogenic RV dysplasia [ARVD]) is a heterogeneous inherited disease that results in fibrofatty infiltration of the right ventriclepredominant, although the disease can also affect the left ventricle (typically the posterior portion). It is a rare and life threatening cause of sudden cardiac death. ECG often carries the first clue to its diagnosis and a high degree of suspicion needs to be maintained to identify this condition in young patients presenting with syncope. We are presenting one such case of an young male who presented with syncope and one episode of documented VT who on evaluation turned out to be a case of ARVD.

Keywords

• ARVD/ARVC
• ventricular arrhythmias
• sudden death
• cardiac MRI
• ICD