Littoral cell angioma of the spleen in a child with Cornelia De Lange syndrome

Abstract

Littoral Cell Angioma (LCA) is a benign and rare vascular tumor of the spleen. It is uncommon in children, and a comprehensive literature review has yielded only 12 published pediatric cases of LCA. Here we present a seven year old, female who was a known case of Cornelia De Lange syndrome who presented with splenic cysts and underwent splenectomy. Histopathological review revealed LCA.

Keywords

• Spleen
• Littoral cell angioma
• Pediatric
• Cornelia De Lange syndrome