Retinitis pigmentosa with concomitant essential iris atrophy and glaucoma – case report

Abstract

Sérgio Henrique Sampaio Meirelles,1–3 Aline Sá Barreto,1 Eduardo Scaldini Buscacio,1,2 Elke Shinzato,1,2,4 Lia Florim Patrão,1 Mauro Sérgio de Oliveira Silva1 1Piedade Municipal Hospital, Rio de Janeiro, 2Federal University of Rio de Janeiro, 3Estacio de Sá University, Rio de Janeiro, Brazil; 4Ocular Ultrasound Department, Clinical Hospital of the University of São Paulo Medical School, São Paulo, Brazil Purpose: To report a case of a young patient with retinitis pigmentosa (RP), essential iris atrophy, and glaucoma.Case report: This report presents a case of a 22-year-old female patient with unilateral glaucoma, increased intraocular pressure, increased cup–disc ratio, iris atrophy, peripheral anterior synechiae, and bilateral RP.Discussion: The patient presented glaucoma due to the iridocorneal endothelial syndrome, despite low age. RP is a bilateral disorder that may be associated with angle-closure glaucoma. Keywords: ocular hypertension, ICE syndrome, secondary glaucoma, retinal degeneration