Sapho syndrome. Tune-up on a clinical case in the CHPR.

Abstract

Sapho syndrome involves synovitis, acne, pustulosis, hiperostosis and osteitis. It is recognized since 1987 as a sero negative spondiloartrhopaty. Sapho´s most importante characteristic is the association between specific dermatological and osteoarticular inflammatory disorders. Recently we diagnosed a 15 years old boy with Sapho at the Hospital Pereira Rossell 8 months after his first visit. The purpose of this paper is to review the literature about this uncommon disease in order to provide the medical community the criteria to achieve a rapid diagnose and the correct treatment avoiding invasive maneuvers and unnecessary antibioticotherapy. Sapho diagnosis is mainly clinical and symptomatic treatment is preferred. It is important to explain to the family and patient the benign and auto limited characteristics of the syndrome.

Keywords

• Sapho
• síndrome Sapho
•   sinovitis
• hiperostosis
• pustulosis, osteitis.SAPHO
• SAPHO syndrome
• acne
• synovitis
• osteitis.