Fibrous dysplasia of sphenoid bone presenting as a case of loss of vision

Abstract

Background: Fibrous dysplasia is a fibro-osseous lesion of unclear aetiology wherein normal bone is replaced by abnormal fibrous tissue and immature bone. Fibrous dysplasia is associated with a defect in osteoblastic differentiation and maturation that originates in the mesenchymal precursor of the bone & is well documented to affect craniofacial structures. Case description: A case of the lesser sphenoid wing fibrous dysplasia is described which presented with symptoms of pressure effects on the optic nerve, managed subsequently with microsurgical decompression of the nerve. Conclusion: Craniofacial fibrous dysplasia is an uncommon entity which can present with loss of vision, wherein the visual prognosis depends upon timed & adequate surgical intervention.

Keywords

• fibrous dysplasia
• sphenoid wing
• orbit