Critical Care Explorations (Nov 2021)
Detectable A Disintegrin and Metalloproteinase With Thrombospondin Motifs-1 in Serum Is Associated With Adverse Outcome in Pediatric Sepsis
- Navin P. Boeddha, MD, PhD,
- Gertjan J. Driessen, MD, PhD,
- Nienke N. Hagedoorn, MD,
- Daniela S. Kohlfuerst, MD,
- Clive J. Hoggart, PhD,
- Angelique L. van Rijswijk, MSc,
- Ebru Ekinci, MD,
- Debby Priem, BSc,
- Luregn J. Schlapbach, MD, PhD,
- Jethro A. Herberg, MD, PhD,
- Ronald de Groot, MD, PhD,
- Suzanne T. Anderson, MD, PhD,
- Colin G. Fink, PhD,
- Enitan D. Carrol, MD, PhD,
- Michiel van der Flier, MD, PhD,
- Federico Martinón-Torres, MD, PhD,
- Michael Levin, MD, PhD,
- Frank W. Leebeek, MD, PhD,
- Werner Zenz, MD, PhD,
- Moniek P. M. de Maat, PhD,
- Jan A. Hazelzet, MD, PhD,
- Marieke Emonts, MD, PhD,
- Willem A. Dik, PhD,
- on behalf of the EUCLIDS consortium,
- Michael Levin,
- Lachlan Coin,
- Stuart Gormley,
- Shea Hamilton,
- Jethro Herberg,
- Bernardo Hourmat,
- Clive Hoggart,
- Myrsini Kaforou,
- Vanessa Sancho-Shimizu,
- Victoria Wright,
- Amina Abdulla,
- Paul Agapow,
- Maeve Bartlett,
- Evangelos Bellos,
- Hariklia Eleftherohorinou,
- Rachel Galassini,
- David Inwald,
- Meg Mashbat,
- Stefanie Menikou,
- Sobia Mustafa,
- Simon Nadel,
- Rahmeen Rahman,
- Clare Thakker,
- S Bokhandi,
- Sue Power,
- Heather Barham,
- N Pathan,
- Jenna Ridout,
- Deborah White,
- Sarah Thurston,
- S Faust,
- S Patel,
- Jenni McCorkell,
- P Davies,
- Lindsey Crate,
- Helen Navarra,
- Stephanie Carter,
- R Ramaiah,
- Rekha Patel,
- Catherine Tuffrey,
- Andrew Gribbin,
- Sharon McCready,
- Mark Peters,
- Katie Hardy,
- Fran Standing,
- Lauren O’Neill,
- Eugenia Abelake,
- Akash Deep,
- Eniola Nsirim,
- A Pollard,
- Louise Willis,
- Zoe Young,
- C Royad,
- Sonia White,
- PM Fortune,
- Phil Hudnott,
- Federico Martinón-Torres,
- Antonio Salas,
- Fernando Álvez González,
- Ruth Barral-Arca,
- Miriam Cebey-López,
- María José CurrasTuala,
- Natalia García,
- Luisa García Vicente,
- Alberto Gómez-Carballa,
- Jose Gómez Rial,
- Andrea Grela Beiroa,
- Antonio Justicia Grande,
- Pilar Leboráns Iglesias,
- Alba Elena Martínez Santos,
- Federico Martinón-Torres,
- Nazareth Martinón-Torres,
- José María Martinón Sánchez,
- Beatriz Morillo Gutiérrez,
- Belén Mosquera Pérez,
- Pablo Obando Pacheco,
- Jacobo Pardo-Seco,
- Sara Pischedda,
- Irene Rivero Calle,
- Carmen Rodríguez-Tenreiro,
- Lorenzo Redondo-Collazo,
- Antonio Salas Ellacuriaga,
- Sonia Serén Fernández,
- María del Sol Porto Silva,
- Ana Vega,
- Lucía Vilanova Trillo,
- Susana Beatriz Reyes,
- María Cruz León León,
- Álvaro Navarro Mingorance,
- Xavier Gabaldó Barrios,
- Eider Oñate Vergara,
- Andrés Concha Torre,
- Ana Vivanco,
- Reyes Fernández,
- Francisco Giménez Sánchez,
- Miguel Sánchez Forte,
- Pablo Rojo,
- J.Ruiz Contreras,
- Alba Palacios,
- Cristina Epalza Ibarrondo,
- Elizabeth Fernández Cooke,
- Marisa Navarro,
- Cristina Álvarez Álvarez,
- María José Lozano,
- Eduardo Carreras,
- Sonia Brió Sanagustín,
- Olaf Neth,
- Mª del Carmen Martínez Padilla,
- Luis Manuel Prieto Tato,
- Sara Guillén,
- Laura Fernández Silveira,
- David Moreno,
- R. de Groot,
- A.M. Tutu van Furth,
- M. van der Flier,
- N.P. Boeddha,
- G.J.A. Driessen,
- M. Emonts,
- J.A. Hazelzet,
- T.W. Kuijpers,
- D. Pajkrt,
- E.A.M. Sanders,
- D. van de Beek,
- A. van der Ende,
- H.L.A. Philipsen,
- A.O.A. Adeel,
- M.A. Breukels,
- D.M.C. Brinkman,
- C.C.M.M. de Korte,
- E. de Vries,
- W.J. de Waal,
- R. Dekkers,
- A. Dings-Lammertink,
- R.A. Doedens,
- A.E. Donker,
- M. Dousma,
- T.E. Faber,
- G.P.J.M. Gerrits,
- J.A.M. Gerver,
- J. Heidema,
- J. Homan-van der Veen,
- M.A.M. Jacobs,
- N.J.G. Jansen,
- P. Kawczynski,
- K. Klucovska,
- M.C.J. Kneyber,
- Y. Koopman-Keemink,
- V.J. Langenhorst,
- J. Leusink,
- B.F. Loza,
- I.T. Merth,
- C.J. Miedema,
- C. Neeleman,
- J.G. Noordzij,
- C.C. Obihara,
- A.L.T. van Overbeek – van Gils,
- G.H. Poortman,
- S.T. Potgieter,
- J. Potjewijd,
- P.P.R. Rosias,
- T. Sprong,
- G.W. ten Tussher,
- B.J. Thio,
- G.A. Tramper-Strander,
- M. van Deuren,
- H. van der Meer,
- A.J.M. van Kuppevelt,
- A.M. van Wermeskerken,
- W.A. Verwijs,
- T.F.W. Wolfs,
- Luregn J Schlapbach,
- Philipp Agyeman,
- Christoph Aebi,
- Eric Giannoni,
- Martin Stocker,
- Klara M Posfay-Barbe,
- Ulrich Heininger,
- Sara Bernhard-Stirnemann,
- Anita Niederer-Loher,
- Christian Kahlert,
- Paul Hasters,
- Christa Relly,
- Walter Baer,
- Christoph Berger,
- Enitan Carrol,
- Stéphane Paulus,
- Hannah Frederick,
- Rebecca Jennings,
- Joanne Johnston,
- Rhian Kenwright,
- Colin G Fink,
- Elli Pinnock,
- Marieke Emonts,
- Rachel Agbeko,
- Suzanne Anderson,
- Fatou Secka,
- Kalifa Bojang,
- Isatou Sarr,
- Ngane Kebbeh,
- Gibbi Sey,
- Momodou Saidykhan,
- Fatoumatta Cole,
- Gilleh Thomas,
- Martin Antonio,
- Werner Zenz,
- Daniela S. Klobassa,
- Alexander Binder,
- Nina A. Schweintzger,
- Manfred Sagmeister,
- Hinrich Baumgart,
- Markus Baumgartner,
- Uta Behrends,
- Ariane Biebl,
- Robert Birnbacher,
- Jan-Gerd Blanke,
- Carsten Boelke,
- Kai Breuling,
- Jürgen Brunner,
- Maria Buller,
- Peter Dahlem,
- Beate Dietrich,
- Ernst Eber,
- Johannes Elias,
- Josef Emhofer,
- Rosa Etschmaier,
- Sebastian Farr,
- Ylenia Girtler,
- Irina Grigorow,
- Konrad Heimann,
- Ulrike Ihm,
- Zdenek Jaros,
- Hermann Kalhoff,
- Wilhelm Kaulfersch,
- Christoph Kemen,
- Nina Klocker,
- Bernhard Köster,
- Benno Kohlmaier,
- Eleni Komini,
- Lydia Kramer,
- Antje Neubert,
- Daniel Ortner,
- Lydia Pescollderungg,
- Klaus Pfurtscheller,
- Karl Reiter,
- Goran Ristic,
- Siegfried Rödl,
- Andrea Sellner,
- Astrid Sonnleitner,
- Matthias Sperl,
- Wolfgang Stelzl,
- Holger Till,
- Andreas Trobisch,
- Anne Vierzig,
- Ulrich Vogel,
- Christina Weingarten,
- Stefanie Welke,
- Andreas Wimmer,
- Uwe Wintergerst,
- Daniel Wüller,
- Andrew Zaunschirm,
- Ieva Ziuraite,
- Veslava Žukovskaja
Affiliations
- Navin P. Boeddha, MD, PhD
- 1 Intensive Care and Department of Pediatric Surgery, Erasmus MC-Sophia Children’s Hospital, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- Gertjan J. Driessen, MD, PhD
- 3 Department of Paediatrics, Maastricht University Medical Center, Maastricht, The Netherlands.
- Nienke N. Hagedoorn, MD
- 2 Department of Pediatrics, Erasmus MC-Sophia Children’s Hospital, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- Daniela S. Kohlfuerst, MD
- 4 Department of General Paediatrics, Medical University of Graz, Graz, Austria.
- Clive J. Hoggart, PhD
- 5 Section of Pediatrics, Imperial College London, London, United Kingdom.
- Angelique L. van Rijswijk, MSc
- 7 Laboratory Medical Immunology, Department of Immunology, Erasmus MC, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- Ebru Ekinci, MD
- 2 Department of Pediatrics, Erasmus MC-Sophia Children’s Hospital, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- Debby Priem, BSc
- 8 Department of Hematology, Erasmus MC, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- Luregn J. Schlapbach, MD, PhD
- 9 Child Health Research Center, The University of Queensland, Brisbane, QLD, Australia.
- Jethro A. Herberg, MD, PhD
- 5 Section of Pediatrics, Imperial College London, London, United Kingdom.
- Ronald de Groot, MD, PhD
- 12 Radboudumc Technology Center Clinical Studies, Radboudumc, Nijmegen, The Netherlands.
- Suzanne T. Anderson, MD, PhD
- 15 MRC Unit The Gambia at the LSHTM, Banjul, The Gambia.
- Colin G. Fink, PhD
- 16 Micropathology Ltd, University of Warwick Science Park, Venture Centre, Coventry, United Kingdom.
- Enitan D. Carrol, MD, PhD
- 17 Institute of Infection, Veterinary and Ecological Sciences, University of Liverpool, Liverpool, United Kingdom.
- Michiel van der Flier, MD, PhD
- 18 Paediatric Infectious Diseases and Immunology, Wilhelmina Children’s Hospital, UMC Utrecht, Utrecht, The Netherlands.
- Federico Martinón-Torres, MD, PhD
- 20 Translational Pediatrics and Infectious Diseases Section, Pediatrics Department, Hospital Clínico Universitario de Santiago de Compostela, Santiago de Compostela, Spain.
- Michael Levin, MD, PhD
- 5 Section of Pediatrics, Imperial College London, London, United Kingdom.
- Frank W. Leebeek, MD, PhD
- 8 Department of Hematology, Erasmus MC, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- Werner Zenz, MD, PhD
- 4 Department of General Paediatrics, Medical University of Graz, Graz, Austria.
- Moniek P. M. de Maat, PhD
- 8 Department of Hematology, Erasmus MC, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- Jan A. Hazelzet, MD, PhD
- 22 Department of Public Health, Erasmus MC, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- Marieke Emonts, MD, PhD
- 23 Paediatric Infectious Diseases and Immunology Department, Great North Children’s Hospital, Newcastle upon Tyne Hospitals NHS Foundation Trust, Newcastle upon Tyne, United Kingdom.
- Willem A. Dik, PhD
- 7 Laboratory Medical Immunology, Department of Immunology, Erasmus MC, University Medical Center Rotterdam, Rotterdam, The Netherlands.
- on behalf of the EUCLIDS consortium
- Michael Levin
- Lachlan Coin
- Stuart Gormley
- Shea Hamilton
- Jethro Herberg
- Bernardo Hourmat
- Clive Hoggart
- Myrsini Kaforou
- Vanessa Sancho-Shimizu
- Victoria Wright
- Amina Abdulla
- Paul Agapow
- Maeve Bartlett
- Evangelos Bellos
- Hariklia Eleftherohorinou
- Rachel Galassini
- David Inwald
- Meg Mashbat
- Stefanie Menikou
- Sobia Mustafa
- Simon Nadel
- Rahmeen Rahman
- Clare Thakker
- S Bokhandi
- Sue Power
- Heather Barham
- N Pathan
- Jenna Ridout
- Deborah White
- Sarah Thurston
- S Faust
- S Patel
- Jenni McCorkell
- P Davies
- Lindsey Crate
- Helen Navarra
- Stephanie Carter
- R Ramaiah
- Rekha Patel
- Catherine Tuffrey
- Andrew Gribbin
- Sharon McCready
- Mark Peters
- Katie Hardy
- Fran Standing
- Lauren O’Neill
- Eugenia Abelake
- Akash Deep
- Eniola Nsirim
- A Pollard
- Louise Willis
- Zoe Young
- C Royad
- Sonia White
- PM Fortune
- Phil Hudnott
- Federico Martinón-Torres
- Antonio Salas
- Fernando Álvez González
- Ruth Barral-Arca
- Miriam Cebey-López
- María José CurrasTuala
- Natalia García
- Luisa García Vicente
- Alberto Gómez-Carballa
- Jose Gómez Rial
- Andrea Grela Beiroa
- Antonio Justicia Grande
- Pilar Leboráns Iglesias
- Alba Elena Martínez Santos
- Federico Martinón-Torres
- Nazareth Martinón-Torres
- José María Martinón Sánchez
- Beatriz Morillo Gutiérrez
- Belén Mosquera Pérez
- Pablo Obando Pacheco
- Jacobo Pardo-Seco
- Sara Pischedda
- Irene Rivero Calle
- Carmen Rodríguez-Tenreiro
- Lorenzo Redondo-Collazo
- Antonio Salas Ellacuriaga
- Sonia Serén Fernández
- María del Sol Porto Silva
- Ana Vega
- Lucía Vilanova Trillo
- Susana Beatriz Reyes
- María Cruz León León
- Álvaro Navarro Mingorance
- Xavier Gabaldó Barrios
- Eider Oñate Vergara
- Andrés Concha Torre
- Ana Vivanco
- Reyes Fernández
- Francisco Giménez Sánchez
- Miguel Sánchez Forte
- Pablo Rojo
- J.Ruiz Contreras
- Alba Palacios
- Cristina Epalza Ibarrondo
- Elizabeth Fernández Cooke
- Marisa Navarro
- Cristina Álvarez Álvarez
- María José Lozano
- Eduardo Carreras
- Sonia Brió Sanagustín
- Olaf Neth
- Mª del Carmen Martínez Padilla
- Luis Manuel Prieto Tato
- Sara Guillén
- Laura Fernández Silveira
- David Moreno
- R. de Groot
- A.M. Tutu van Furth
- M. van der Flier
- N.P. Boeddha
- G.J.A. Driessen
- M. Emonts
- J.A. Hazelzet
- T.W. Kuijpers
- D. Pajkrt
- E.A.M. Sanders
- D. van de Beek
- A. van der Ende
- H.L.A. Philipsen
- A.O.A. Adeel
- M.A. Breukels
- D.M.C. Brinkman
- C.C.M.M. de Korte
- E. de Vries
- W.J. de Waal
- R. Dekkers
- A. Dings-Lammertink
- R.A. Doedens
- A.E. Donker
- M. Dousma
- T.E. Faber
- G.P.J.M. Gerrits
- J.A.M. Gerver
- J. Heidema
- J. Homan-van der Veen
- M.A.M. Jacobs
- N.J.G. Jansen
- P. Kawczynski
- K. Klucovska
- M.C.J. Kneyber
- Y. Koopman-Keemink
- V.J. Langenhorst
- J. Leusink
- B.F. Loza
- I.T. Merth
- C.J. Miedema
- C. Neeleman
- J.G. Noordzij
- C.C. Obihara
- A.L.T. van Overbeek – van Gils
- G.H. Poortman
- S.T. Potgieter
- J. Potjewijd
- P.P.R. Rosias
- T. Sprong
- G.W. ten Tussher
- B.J. Thio
- G.A. Tramper-Strander
- M. van Deuren
- H. van der Meer
- A.J.M. van Kuppevelt
- A.M. van Wermeskerken
- W.A. Verwijs
- T.F.W. Wolfs
- Luregn J Schlapbach
- Philipp Agyeman
- Christoph Aebi
- Eric Giannoni
- Martin Stocker
- Klara M Posfay-Barbe
- Ulrich Heininger
- Sara Bernhard-Stirnemann
- Anita Niederer-Loher
- Christian Kahlert
- Paul Hasters
- Christa Relly
- Walter Baer
- Christoph Berger
- Enitan Carrol
- Stéphane Paulus
- Hannah Frederick
- Rebecca Jennings
- Joanne Johnston
- Rhian Kenwright
- Colin G Fink
- Elli Pinnock
- Marieke Emonts
- Rachel Agbeko
- Suzanne Anderson
- Fatou Secka
- Kalifa Bojang
- Isatou Sarr
- Ngane Kebbeh
- Gibbi Sey
- Momodou Saidykhan
- Fatoumatta Cole
- Gilleh Thomas
- Martin Antonio
- Werner Zenz
- Daniela S. Klobassa
- Alexander Binder
- Nina A. Schweintzger
- Manfred Sagmeister
- Hinrich Baumgart
- Markus Baumgartner
- Uta Behrends
- Ariane Biebl
- Robert Birnbacher
- Jan-Gerd Blanke
- Carsten Boelke
- Kai Breuling
- Jürgen Brunner
- Maria Buller
- Peter Dahlem
- Beate Dietrich
- Ernst Eber
- Johannes Elias
- Josef Emhofer
- Rosa Etschmaier
- Sebastian Farr
- Ylenia Girtler
- Irina Grigorow
- Konrad Heimann
- Ulrike Ihm
- Zdenek Jaros
- Hermann Kalhoff
- Wilhelm Kaulfersch
- Christoph Kemen
- Nina Klocker
- Bernhard Köster
- Benno Kohlmaier
- Eleni Komini
- Lydia Kramer
- Antje Neubert
- Daniel Ortner
- Lydia Pescollderungg
- Klaus Pfurtscheller
- Karl Reiter
- Goran Ristic
- Siegfried Rödl
- Andrea Sellner
- Astrid Sonnleitner
- Matthias Sperl
- Wolfgang Stelzl
- Holger Till
- Andreas Trobisch
- Anne Vierzig
- Ulrich Vogel
- Christina Weingarten
- Stefanie Welke
- Andreas Wimmer
- Uwe Wintergerst
- Daniel Wüller
- Andrew Zaunschirm
- Ieva Ziuraite
- Veslava Žukovskaja
- DOI
- https://doi.org/10.1097/CCE.0000000000000569
- Journal volume & issue
-
Vol. 3,
no. 11
p. e0569
Abstract
IMPORTANCE:. A Disintegrin and Metalloproteinase with Thrombospondin Motifs-1 is hypothesized to play a role in the pathogenesis of invasive infection, but studies in sepsis are lacking. OBJECTIVES:. To study A Disintegrin and Metalloproteinase with Thrombospondin Motifs-1 protein level in pediatric sepsis and to study the association with outcome. DESIGN:. Data from two prospective cohort studies. SETTING AND PARTICIPANTS:. Cohort 1 is from a single-center study involving children admitted to PICU with meningococcal sepsis (samples obtained at three time points). Cohort 2 includes patients from a multicenter study involving children admitted to the hospital with invasive bacterial infections of differing etiologies (samples obtained within 48 hr after hospital admission). MAIN OUTCOMES AND MEASURES:. Primary outcome measure was mortality. Secondary outcome measures were PICU-free days at day 28 and hospital length of stay. RESULTS:. In cohort 1 (n = 59), nonsurvivors more frequently had A Disintegrin and Metalloproteinase with Thrombospondin Motifs-1 levels above the detection limit than survivors at admission to PICU (8/11 [73%] and 6/23 [26%], respectively; p = 0.02) and at t = 24 hours (2/3 [67%] and 3/37 [8%], respectively; p = 0.04). In cohort 2 (n = 240), A Disintegrin and Metalloproteinase with Thrombospondin Motifs-1 levels in patients within 48 hours after hospital admission were more frequently above the detection limit than in healthy controls (110/240 [46%] and 14/64 [22%], respectively; p = 0.001). Nonsurvivors more often had detectable A Disintegrin and Metalloproteinase with Thrombospondin Motifs-1 levels than survivors (16/21 [76%] and 94/219 [43%], respectively; p = 0.003), which was mostly attributable to patients with Neisseria meningitidis. CONCLUSIONS AND RELEVANCE:. In children with bacterial infection, detection of A Disintegrin and Metalloproteinase with Thrombospondin Motifs-1 within 48 hours after hospital admission is associated with death, particularly in meningococcal sepsis. Future studies should confirm the prognostic value of A Disintegrin and Metalloproteinase with Thrombospondin Motifs-1 and should study pathophysiologic mechanisms.