Isolated unilateral pulmonary artery atresia with contralateral pulmonary artery branch stenosis: A “window” for intervention

Abstract

Adult presentation of unilateral pulmonary artery atresia in association with contralateral branch pulmonary stenosis is rare. We present the case of a quadragenarian, who manifested with right ventricular failure and hemoptysis. This report discusses the diagnostic workup and therapeutic options along with a brief overview of the concerned literature.

Keywords

• adult-onset congenital heart disease
• multimodality imaging
• peripheral pulmonary stenosis
• pulmonary angioplasty
• unilateral pulmonary artery atresia