Role of Septal Myectomy in Pediatric Hypertrophic Cardiomyopathy

Abstract

Hypertrophic cardiomyopathy is a prevalent cause of sudden cardiac death among young people. This distinctive genetic condition can manifest at any age from infancy to adulthood. The primary features include unexplained left ventricular hypertrophy coupled with dynamic left ventricular outflow tract (LVOT) obstruction and a variable degree of mitral valve regurgitation. In certain cases, patients may also experience biventricular outflow tract obstruction. Surgical septal myectomy is the gold standard treatment for symptomatic children experiencing severe LVOT obstruction. This review focuses on surgical techniques for septal myectomy in pediatric patients and other adjunct procedures and summarizes the current outcomes.

Keywords

• hypertrophic cardiomyopathy
• sudden cardiac death
• left ventricular outflow tract obstruction
• asymmetrical septal hypertrophy
• left ventricular myectomy