A case of portal biliopathy in a young patient with portal cavernoma secondary to neonatal umbilical vein catheterization

Abstract

Portal biliopathy (PB) refers to biliary obstruction caused by cavernous transformation of the portal vein (CTPV). CTPV occurs most frequently in patients with liver cirrhosis or malignancy. Less common causes include congenital malformations and neonatal umbilical vein cannulation. We present a case of portal biliopathy in a 28-year-old man with CTPV secondary to umbilical vein catheterization in neonatal age. The case illustrates portal biliopathy as a late complication of neonatal invasive procedures and highlights the importance of a multimodality imaging approach to achieve a prompt diagnosis.

Keywords

• Portal cavernoma
• Biliary disease
• Bile duct diseases
• Cholestasis in children
• Portal vein obstruction
• Interventional endoscopy