Untreated patient of Pentalogy of Cantrell surviving into the sixth decade: A unique case report

Abstract

Pentalogy of Cantrell is a rare syndrome consisting of a constellation of congenital anomalies including omphalocoele, lower sternal defect, sdiaphragmatic defect, diaphragmatic pericardial defect and congenital heart disease. It is reported to be usually fatal in absence of timely treatment. We present a case where an untreated patient has miraculously survived into the sixth decade.

Keywords

• Pentalogy of cantrell
• Omphalocoele
• Ventricular aneurysm
• MDCT
• Sternal defect