Solid pseudopapillary neoplasm of the pancreas

Abstract

Solid pseudopapillary neoplasm of the pancreas (SPN) is a very rare tumor with a low malignant potential. Although most commonly presenting in females in the second to fourth decade of life, it has been reported in the pediatric population with an incidence of 8–16.6%. SPN was first described by Virginia Kneeland Frantz in 1959 as a papillary cystic tumor of the pancreas in a 2 year old male patient. Herein we report 2 cases of SPN and review the pathophysiology, diagnosis, and management. Keywords: Solid pseudopapillary neoplasm, Frantz tumor, Pancreatic tumor