A rare case of wegeners granulomatosis with allergic bronchopulmonary aspergillosis in a child

Abstract

Wegener’s granulomatosis is an uncommon autoimmue disease with multi-system involvement, characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tracts and general focal necrotizing vasculitis (Commonly known as Wegener’s triad). The lungs are involved in 72 percents of patients and the clinical and radiographic findings indicate bilateral pulmonary nodules of varying size and definition, cavitated in half of the patients, accompanied by the nodular lesion with rare involvement of the pleura. We present a case in 4 year old male child presenting with symptoms of recurrent airway disease and chronic sinusitis with detection of lung lesions on further investigations and pathological confirmation by antineutrophil cytoplasmic antibody positivity and based on radiological and clinical suspicion.

Keywords

• wegener’s granulomatosis
• lung cavitation
• anca