Left Ventricular Noncompaction: Often Forgotten Cause of Heart Failure

Abstract

Left ventricular (LV) noncompaction is a form of genetic cardiomyopathy characterized by hypertrabeculations with deep intertrabecular recesses of the LV myocardium. The diagnosis can be confirmed by echocardiography and magnetic resonance imaging. These patients can be asymptomatic or may present with heart failure, arrhythmias, or thromboembolic episodes. The management is guideline directed. When associated with congenital heart defects or correctable valvular lesions, surgical management should be advised. Familial screening and counseling of first-degree relatives are essential. In this review, an attempt has been made to give an overview of this condition.

Keywords

• cardiac magnetic resonance imaging
• heart failure
• left ventricular dysfunction
• noncompaction cardiomyopathy