A rare variant of intracardiac total anomalous pulmonary venous connection

Abstract

Total anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. We present an interesting case of TAPVC in a patient with situs solitus that connected to the right atrium via a broad-mouthed common chamber. Resumo: As variantes de retorno venoso pulmonar anómalo total (RVPAT) que resultam de conexão e de drenagem direta das veias pulmonares à aurícula morfologicamente direita são extremamente raras, exceto no caso de presença de isomerismo direito. Apresentamos um caso de RVPAT, com drenagem à aurícula direita através de um coletor comum, num doente com situs solitus. Keywords: Total anomalous pulmonary venous connection, Cardiac total anomalous pulmonary venous connection, Supracardiac total anomalous pulmonary venous connection, Palavras-chave: Conexão anómala total das veias pulmonares, Conexão anómala total de veias pulmonares cardíaca, Conexão anómala total de veias pulmonares supracardíaca