Российский кардиологический журнал (Feb 2017)

NON-COMPACTION LEFT VENTRICLE MYOCARDIUM: A SYMPTOM, SYNDROME OR DEVELOPMENT VARIATION?

  • M. E. Polyak,
  • E. A. Mershina,
  • E. V. Zaklyazminskaya

DOI
https://doi.org/10.15829/1560-4071-2017-2-106-113
Journal volume & issue
Vol. 0, no. 2
pp. 106 – 113

Abstract

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The left ventricle non-compaction myocardium syndrome is relatively new diagnosis entered clinical practice with improvement of the heart visualization methods. There is plenty of studies on genetic heterogeneity of non-compaction myocardium syndrome and its impact on a variety of associated cardiomyopathies. However, there is no single opinion on pathogenesis of non-compaction, as there are no unified diagnostic criteria and no guideline on treatment and management of patients with this syndrome. Current review provides a summary of data on this pathology nature, its genetics, diagnostics and treatment.

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