Chronic renal failure as initial presentation of pelvic hemangioendothelioma.

Abstract

Hemangioendothelioma is a rare vascular tumor whose etiology has not yet been defined. Currently, it is known to affect different sites, such as the abdominal-pelvic cavity. It is also known to present intermediate characteristics to hemangioma and angiosarcoma. In recent studies, 50-76% of patients are asymptomatic. Surgical treatment is indicated in most cases. The authors present a case of hemangioendothelioma with pelvic involvement and initial presentation as acute renal failure due to extrinsic ureteral compression, treated surgically, with histopathological diagnosis of hemangioendothelioma and recurrence after one year of the initial treatment presenting a histologically different form. This case illustrates a rare cause of lower urinary tract symptoms (LUTS), obstructive uropathy and acute renal failure and the appearance of two different tumors within a year, in line with the genetic/immunological factor in its genesis.

Keywords

• hemangioendothelioma
• sarcoma
• myxoid liposarcoma
• chronic renal failure.