Right Sided Aortic Arch and its Rare Associations- A Case Series

Abstract

Right sided aortic arch is a rare incidental anomaly in adults often asymptomatic. Most common subtype is Right Aortic Arch (RAA) with aberrant left subclavian artery. We report three cases of right sided aortic arch with multiple vascular anomalies. Two cases were showing mirror image branching with situs inversus totalis and Tetrology of Fallot (TOF). Another one showing retroesophageal circumflex aorta with aberrant left subclavian artery ,supra-sinus origin of coronary arteries, bicuspid aortic valve, Persistant Left Superior Vena Cava (PLSVC) and Autosomal Dominant Polycystic Kidney Disease (ADPKD). Through cross sectional CT angiography of the aortic arch and surrounding structures, we defined anatomical relationships, which is useful for follow-up and treatment.

Keywords

• mirror image branching
• retroesophageal circumflex aorta
• situs inversus totalis
• tetrology of fallot