Idiopathic pleuroparenchymal fibroelastosis: a rare case report

Hajar Hamri; Zakaria Toufga; Sanae Chaoui; Hounaida Jerguigue; Rachida Latib; Youssef Omor

doi:10.11604/pamj-cm.2020.3.34.23176

PAMJ Clinical Medicine (Jun 2020)

Idiopathic pleuroparenchymal fibroelastosis: a rare case report

Hajar Hamri,
Zakaria Toufga,
Sanae Chaoui,
Hounaida Jerguigue,
Rachida Latib,
Youssef Omor

Affiliations

Hajar Hamri: Imaging Department, National Institute of Oncology, Mohammed V University, Rabat, Morocco
Zakaria Toufga: Imaging Department, National Institute of Oncology, Mohammed V University, Rabat, Morocco
Sanae Chaoui: Imaging Department, National Institute of Oncology, Mohammed V University, Rabat, Morocco
Hounaida Jerguigue: Imaging Department, National Institute of Oncology, Mohammed V University, Rabat, Morocco
Rachida Latib: Imaging Department, National Institute of Oncology, Mohammed V University, Rabat, Morocco
Youssef Omor: Imaging Department, National Institute of Oncology, Mohammed V University, Rabat, Morocco

DOI: https://doi.org/10.11604/pamj-cm.2020.3.34.23176
Journal volume & issue: Vol. 3, no. 34

Abstract

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Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare clinical-pathologic entity characterized by fibrotic thickening of the pleural and subpleural parenchyma predominantly in the upper lobes. The clinical course of the disease is progressive and the prognosis is poor. The only therapeutic option is lung transplantation. We report a case fulfilling the criteria of IPPFE in a 47-year-old female, in order to review the CT and clinical aspects as well as the differential diagnoses of this disorder.

Published in PAMJ Clinical Medicine

ISSN: 2707-2797 (Online)
Publisher: PAMJ
Country of publisher: Kenya
LCC subjects: Medicine
Website: https://clinical-medicine.panafrican-med-journal.com/

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Abstract

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