PHAKOMATOSIS PIGMENTOVASCULARIS: REPORT OF A CASE

Abstract

The present study introduces a rare case of phakomatosispigmenJovascularis, which is charaderiud by the existence ofpigmentary naevus ond vascular naevus. Until 1985, 63 cases ofthis syndrome have been reported, mostly in Japon (56 cases). This is the first case of phakomatosis pigmentovascularis, reported in Iran.