Brazilian Journal of Anesthesiology (Nov 2022)

Neuraxial block anesthetic technique in a patient with SCN8A encephalopathy: case report

  • Eric Guimar.·es Machado,
  • Isis da Rocha Costa Bill..,
  • Mariana Moraes Pereira das Neves Ara..jo,
  • Jos.. Francisco Nunes Pereira das Neves,
  • Gilson Lorena Mau..s,
  • Marco Felipe Bouzada Marcos,
  • Fernando de Paiva Ara..jo

Journal volume & issue
Vol. 72, no. 6
pp. 826 – 828

Abstract

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Mutations in SCN8A gene lead to changes in sodium channels in the brain, which are correlated with severe epileptic syndrome. Due to the rarity, there are few studies that support anesthesia in that population. The present study aims to report alternatives to inhalation anesthesia at epileptic encephalopathy. Case report: Male, 4 years old, with SCN8A encephalopathy with surgical indication of orchidopexy. Neuroaxis block was performed and dexmedetomidine was used as a pre-anesthetic and sedation. The anestheticsurgical act was uneventful. Conclusion: The association of neuraxial block and dexmedetomidine proved to be a viable alternative for surgery in patients with SCN8A encephalopathy.

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