A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease

Hirokazu Touge; Katsuyuki Tomita; Akira Yamasaki; Eiji Shimizu

doi:10.1016/j.rmcr.2017.01.001

Respiratory Medicine Case Reports (Jan 2017)

A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease

Hirokazu Touge,
Katsuyuki Tomita,
Akira Yamasaki,
Eiji Shimizu

Affiliations

Hirokazu Touge: Department of Respiratory Medicine, Yonago Medical Centre, Tottori, Japan
Katsuyuki Tomita: Department of Respiratory Medicine, Yonago Medical Centre, Tottori, Japan
Akira Yamasaki: Division of Medical Oncology and Molecular Respirology, Tottori University Faculty of Medicine, Tottori, Japan
Eiji Shimizu: Division of Medical Oncology and Molecular Respirology, Tottori University Faculty of Medicine, Tottori, Japan

DOI: https://doi.org/10.1016/j.rmcr.2017.01.001
Journal volume & issue: Vol. 20, no. C
pp. 92 – 94

Abstract

Read online

IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right lower lung field in chest X-ray. Transbronchial lung biopsy resulted in a pathological diagnosis of IgG4-RLD. The condition was improved by hormonal therapy.

Published in Respiratory Medicine Case Reports

ISSN: 2213-0071 (Online)
Publisher: Elsevier
Country of publisher: Netherlands
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Diseases of the respiratory system
Website: http://www.journals.elsevier.com/respiratory-medicine-case-reports/

About the journal

Abstract

Keywords