A child with hypertension and ascitis

Abstract

Caroli disease is a rare disorder characterized by congenital dilatation of the intrahepatic biliary tree and may be associated with polycystic kidney disease. Patients usually present with intermittent abdominal pain, hepatomegaly, and recurrent cholangitis. Renal failure as a presenting complaint of Caroli disease is rare. We present a child with Caroli disease who presented to us with renal failure.

Keywords

• Caroli disease
• cholangitis
• hypertension
• polycystic kidney disease
• renal failure