Dental Management of a Rare Case of Cornelia de Lange Syndrome

Abstract

A six-year-old female patient with Cornelia de Lange Syndrome (CdLS) presented to the Department of Paediatric and Preventive Dentistry with multiple mutilated teeth and an inability to chew, resulting in low food intake. The patient complained of nocturnal pain and disturbed sleep. A behavioural analysis of the child showed that she was introverted, had difficulty in interacting with other children or strangers, and exhibited distinctly negative behaviour, as per Frankel’s behaviour rating scale.

Keywords

• general anesthesia
• full mouth rehabilitation
• mandibular arch
• maxillary arch