DIGITAL ISCHEMIA DUE TO SYSTEMIC SCLEROSIS ASSOCIATED WITH ESSENTIAL THROMBOCYTHEMIA: A CASE REPORT

Abstract

Digital ulcers (DU) are a well-known problem in patients with systemic sclerosis. It is an underestimated complication of the disease causing pain and morbidity. Essential thrombocytosis is another cause of DU. The association of theses two diseases increases the risk of ischemic complications and impairment of hand function which are frequently observed in patients with digital ulcers. This report deals with a 68-year-old patient with rare association of Essential thrombocytosis ,Systemic sclerosis and Raynaud’s phenomenon that was refractory to medical treatment of Systemic sclerosis (illoprost,calcium channel blockers) and improved with hydreaR.

Keywords

• systemic sclerosis
• digital ulcers
• essential thrombocythemia