Epicardial Nodules as the Initial Manifestation of Immunoglobulin G4–Related Pericarditis

Abstract

Immunoglobulin G4 (IgG4)–related pericarditis, an immune-mediated fibro-inflammatory condition, is a rare yet life-threatening disease presenting with constrictive pericarditis. We describe a case of IgG4-related pericarditis presenting with epicardial nodules successfully treated with corticosteroids. This case highlights the clinical significance of assessing IgG4-related pericarditis in the diagnostic workup of pericardial masses. (Level of Difficulty: Advanced.)

Keywords

• cardiac magnetic resonance
• computed tomography
• immunoglobulin G4–related disease
• immunoglobulin G4–related pericarditis
• pericardial effusion