Bilateral congenital cystic adenomatoid malformation, stocker type III with associated findings and review of literature

Abstract

Congenital cystic adenomatoid malformation (CCAM) of the lung, Stocker′s type III is a rare anomaly characterized by replacement of normal pulmonary tissue with cysts of variable size and distribution. We report here a 16-week stillborn fetus with Stocker′s type III bilateral CCAM involving the entire lungs. The additional associated malformations included collapsed nasal bridge, low set ears, malformed ears, absence of neck folds, absence of nipples and areolas, tracheal stenosis, fetal hydrops and small heart. The pathogenesis, radiological findings, pathological findings and prognosis of CCAM are discussed along with review of literature.

Keywords

• Congenital
• cystic adenomatoid malformation
• lung