Case Report: Infant-onset Degos disease with nervous system involvement and a literature review

Abstract

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Degos disease also known as malignant atrophic papulosis (MAP), is an autoinflammatory disease that mainly affects small- to medium-sized arteries. Gastrointestinal and nervous system are most commonly affected systems. Herein, we reported a case of Degos disease with disease onset during infantile and had severe neurological involvement.

Keywords

• Degos disease
• malignant atrophic papulosis
• infantile onset
• neurological involvement
• prognosis