Pigmentary mosaicism and extracutaneous defects: a case report of a rare form of twin spotting

Abstract

Progressive cribriform and zosteriform hyperpigmentation (PCZH) is an uncommon disorder of pigmentation that is believed to be a result of pigmentary mosaicism. In this report, we describe a child with congenital nevus depigmentosus and low intelligence who later developed PCZH by the age of 5 years.

Keywords

• nevus depigmentosus
• pigmentary mosaicism
• progressive cribriform and zosteriform hyperpigmentation
• segmental pigmentation disorders