Cystotoperitoneal shunt surgery during infancy in porencepahalic cyst located in frontal region led to regaining of developmental milestone

Abstract

Porencepahalic cyst is considered as an extremely uncommon developmental disorder of the central nervous system, being characterized by the presence of a fluid-filled cysts or cavities located within the cerebral hemispheres. It can be associated with varied aetiology and can present with a spectrum of clinical presentation varying from asymptomatic to grossly spastic limbs, mental retardation, cognitive impairment and intractable seizure. Extensive Pubmed and Medline search did not yield any result when searched for term “infancy, porencepahalic cyst, cystoperitonreal shunt.” However, clear guideline for management is still lacking. Authors report an interesting case of giant porencepahalic cyst located in the right frontal region in infancy and underwent cystoperitonreal shunt surgery, which lead to good outcome with remarkable recovery of delayed milestones with adequate scholastic performances along with marked diminution in the size of porencepahalic cyst.

Keywords

• porencephaly
• raised intracranial pressure
• cystoperitoneal shunt
• surgery