Radiology Case Reports (Jan 2023)

Zinner's syndrome: Masquerading as pyonephrotic ectopic kidney

  • Faiz Manzar Ansari, MS,
  • Sajad Ahmad Para, MS, MCh,
  • Shashank Singh, MS,
  • Mohammad Saleem Wani, MS, MCh,
  • Arif Hamid Bhat, MS, MCh,
  • Manjul Kumar Maurya, MS

Journal volume & issue
Vol. 18, no. 1
pp. 131 – 134

Abstract

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Zinner's syndrome is a rare developmental anomaly of Wolffian duct, comprising a triad of seminal vesicle cyst, ipsilateral renal agenesis and ejaculatory duct obstruction, first described by Zinner in 1914. Several aberrations have been reported like renal dysplasia, ectopic ureteric orifice in one of the derivatives of Wolffian duct. Usually it presents in second to fourth decade of life with symptoms of urinary bladder irritation/obstruction, cyst distension, ejaculatory duct obstruction. The diagnosis is principally based on imaging studies, usually confirmed by MRI. Treatment is based upon the persistent symptoms or complications related to it. Excision of cyst is gold standard.

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