Radiology Case Reports (Dec 2021)

Alveolar soft part sarcoma of the orbit: A case report

  • Takeshi Oda, MD,
  • Kazufumi Kikuchi, PhD,MD,
  • Osamu Togao, MD,PhD,
  • Shingo Baba, MD,PhD,
  • Masahiro Mizoguchi, MD,PhD,
  • Mika Tanabe, MD,PhD,
  • Mamoru Ito, MD,PhD,
  • Hidetaka Yamamoto, MD,PhD,
  • Kousei Ishigami, MD,PhD,
  • Akio Hiwatashi, MD,PhD

Journal volume & issue
Vol. 16, no. 12
pp. 3766 – 3771

Abstract

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Alveolar soft part sarcoma is a rare soft tissue neoplasm that accounts for approximately 1% of all sarcomas and is usually identified in the extremities in adults. The occurrence of alveolar soft part sarcoma in the orbit is extremely rare, estimated at approximately 5% – 15% among all cases of alveolar soft part sarcoma . Here, we present a case of 29-year-old woman with orbital alveolar soft part sarcoma. We describe the magnetic resonance and F-18 2-fluoro-2-deoxy-D-glucose-position emission tomography/computed tomography findings of this case. This young woman had a spindle-shaped mass. A higher signal compared to the extraocular muscle on T1-weighted images, numerous flow voids on T2-weighted images, and intense enhancement could be key findings of this disease.

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