Prague Medical Report (Jun 2020)

Reversible Cerebral Vasoconstriction Syndrome Associated with a Suprarenal Mass

  • Camila Pantoja-Ruiz,
  • Andrés Ricaurte-Fajardo,
  • María Isabel Ocampo-Navia,
  • Juliana Coral-Casas

DOI
https://doi.org/10.14712/23362936.2020.9
Journal volume & issue
Vol. 121, no. 2
pp. 107 – 113

Abstract

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Reversible cerebral vasoconstriction syndrome (RCVS) is characterised by severe thunderclap headaches (with or without the presence of acute neurological symptoms) and segmental vasoconstriction of cerebral arteries that resolves spontaneously in a period of three months. Cases have been described in the literature with producing and non-producing masses of metanephrines. Within these reports, associations with cavernous haemangioma, medulloblastoma, colon cancer, paraganglioma, pheochromocytoma, uterine fibroids, among others were found. However, no association with adrenal masses which do not produce metanephrines was found. In this context, we reported the case of a woman with this type of tumour associated with RCVS which provided a treatment challenge, as well as we reviewed the literature on cases of RCVS associated with masses.

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