Malignant peripheral nerve sheath tumor of the anterior mediastinum: a rare presentation

Abstract

Malignant peripheral nerve sheath tumor (MPNST) is a rare tumor that accounts for 5% of all thoracic neoplasm usually located in the posterior mediastinum and is generally associated with a poor outcome. We present a case of MPNST of the anterior mediastinum presenting in a rare location leading to diagnostic dilemmas and treated primarily by surgical resection.

Keywords

• malignant peripheral nerve sheath tumor, anterior mediastinum, immunohistochemistry