Metastatic angiosarcoma and Kasabach-Merritt syndrome

Abstract

Angiosarcomas are exceedingly rare tumors that are often difficult to diagnose. Exceptionally unusual is the presentation of these tumors with Kasabach-Merritt Syndrome, a curious form of intratumoral coagulation that can be impossible to distinguish from intravascular coagulation, which is more common. Instant recognition of this clinical association can help making a prompt diagnosis and timely initiation of therapy.

Keywords

• angiosarcoma, Kasabach-Merritt syndrome, disseminated coagulopathy