Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case report

Abstract

Papillon–Lefevre syndrome is a rare autosomal recessive disorder, in which the clinical manifestations are periodontitis which results in premature loss of both deciduous and permanent teeth and palmoplantar keratinization. The palmoplantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at the age of 3 or 4 years. The deciduous teeth frequently fall out by about age five and most of the permanent teeth may also be lost by approximately age 17. In the present case, a young, edentulous male of this syndrome having most the characteristic features was treated by modified complete denture prosthesis considering his young age and low socioeconomic status.

Keywords

• keratoderma
• papillon–lefevre syndrome
• periodontitis