Extranodal Natural Killers/T Cell´s Lymphoma: A case report.

Abstract

Introduction: Extranodal Natural Killers/T Cell´s lymphomas are uncommon diseases with a higher incidence in the regions of East Asia and Central and South America and are associated with the Epstein-Barr virus. These neoplasms have a tendency to affect the facial midline, mainly the nasal and paranasal regions. These diseases develop an angiocentric growth pattern with necrosis. These lymphomas have aggressive behavior and high mortality. Objective: The objective of this work is to present a rare case of NK/T-cell lymphoma, which should be taken into account since its late diagnosis influences the high lethality and poor survival. Case Presentation: Here we present a case of an Extranodal Natural Killers/T Cell´s lymphoma in a 21 years old male with a febrile picture of long-standing evolution (3 months), nasal obstruction, weight loss, and swelling of the zygomatic arch, accompanied by tumor infiltration, destruction of the palate, and purulent discharge through the left eye. The symptoms and signs occurred over a period of approximately 4 months, with a progressive deterioration of the patient. Conclusion: Even though Extranodal Natural Killers/T Cell´s lymphoma is an uncommon disease, it has an aggressive clinical course with poor prognosis and survival. Therefore, it should be considered in the differential diagnosis of nasal or paranasal swelling.

Keywords

• nk/t cell lymphoma, enktl, natural killers, non-hodgkin lymphoma, cancer.