Medial canthal lesions in a man with a scarred wrist: Subcutaneous lymphangiomas in association with Maffucci’s syndrome

Abstract

Maffucci syndrome is characterized by multiple soft tissue hemangiomas and multiple enchondromas. Ollier disease includes enchondromatosis without hemangiomas and these two conditions are now thought to represent a spectrum of congenital mesenchymal dysplasia. We present a case of a 49 year-old male affected by multiple enchondromas, who was reclassified as a Maffucci lymphangioma syndrome after two periocular lymphangiomas were surgically excised.

Keywords

• lymphangiomas, Maffucci’s syndrome, enchondromas, Ollier syndrome