Frontiers in Medicine (Dec 2023)
Efficacy of canakinumab in patients with Still’s disease across different lines of biologic therapy: real-life data from the International AIDA Network Registry for Still’s Disease
- Antonio Vitale,
- Antonio Vitale,
- Valeria Caggiano,
- Valeria Caggiano,
- Petros P. Sfikakis,
- Lorenzo Dagna,
- Lorenzo Dagna,
- Giuseppe Lopalco,
- Gaafar Ragab,
- Gaafar Ragab,
- Francesco La Torre,
- Ibrahim A. Almaghlouth,
- Ibrahim A. Almaghlouth,
- Maria Cristina Maggio,
- Jurgen Sota,
- Jurgen Sota,
- Abdurrahman Tufan,
- Andrea Hinojosa-Azaola,
- Florenzo Iannone,
- Roberta Loconte,
- Katerina Laskari,
- Haner Direskeneli,
- Piero Ruscitti,
- Maria Morrone,
- Henrique A. Mayrink Giardini,
- Alexandros Panagiotopoulos,
- Ilenia Di Cola,
- Eduardo Martín-Nares,
- Sara Monti,
- Sara Monti,
- Ludovico De Stefano,
- Ludovico De Stefano,
- Rıza Can Kardas,
- Rahime Duran,
- Corrado Campochiaro,
- Corrado Campochiaro,
- Alessandro Tomelleri,
- Alessandro Tomelleri,
- Abdulaziz Mohammed Alabdulkareem,
- Carla Gaggiano,
- Carla Gaggiano,
- Maria Tarsia,
- Maria Tarsia,
- Elena Bartoloni,
- Mery Romeo,
- Mohamed A. Hussein,
- Ahmed Hatem Laymouna,
- Isabele Parente de Brito Antonelli,
- Marilia Ambiel Dagostin,
- Lampros Fotis,
- Sara Bindoli,
- Luca Navarini,
- Luca Navarini,
- Fatma Alibaz-Oner,
- Gizem Sevik,
- Micol Frassi,
- Francesco Ciccia,
- Daniela Iacono,
- Francesca Crisafulli,
- Piero Portincasa,
- Nour Jaber,
- Perla Ayumi Kawakami-Campos,
- Ewa Wiesik-Szewczyk,
- Annamaria Iagnocco,
- Gabriele Simonini,
- Paolo Sfriso,
- Alberto Balistreri,
- Roberto Giacomelli,
- Roberto Giacomelli,
- Giovanni Conti,
- Bruno Frediani,
- Bruno Frediani,
- Claudia Fabiani,
- Claudia Fabiani,
- Luca Cantarini,
- Luca Cantarini
Affiliations
- Antonio Vitale
- Department of Medical Sciences, Surgery and Neurosciences, Research Center of Systemic Autoinflammatory Diseases and Behçet's Disease Clinic, University of Siena, Siena, Italy
- Antonio Vitale
- Azienda Ospedaliero-Universitaria Senese, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Siena, Italy
- Valeria Caggiano
- Department of Medical Sciences, Surgery and Neurosciences, Research Center of Systemic Autoinflammatory Diseases and Behçet's Disease Clinic, University of Siena, Siena, Italy
- Valeria Caggiano
- Azienda Ospedaliero-Universitaria Senese, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Siena, Italy
- Petros P. Sfikakis
- Joint Academic Rheumatology Program, Medical School, National and Kapodistrian University of Athens, Athens, Greece
- Lorenzo Dagna
- Division of Immunology, Transplants and Infectious Diseases, Università Vita-Salute San Raffaele, Milan, Italy
- Lorenzo Dagna
- Unit of Immunology, Rheumatology, Allergy and Rare Diseases, IRCCS Ospedale San Raffaele, Milan, Italy
- Giuseppe Lopalco
- Department of Precision and Regenerative Medicine and Ionian Area (DiMePRe-J) Policlinic Hospital, University of Bari, Bari, Italy
- Gaafar Ragab
- Rheumatology and Clinical Immunology Unit, Internal Medicine Department, Faculty of Medicine, Cairo University, Giza, Egypt
- Gaafar Ragab
- Faculty of Medicine, Newgiza University, 6th of October City, Egypt
- Francesco La Torre
- Department of Pediatrics, Pediatric Rheumatology Center, Giovanni XXIII Pediatric Hospital, University of Bari, Bari, Italy
- Ibrahim A. Almaghlouth
- 0Rheumatology Unit, Department of Medicine, College of Medicine, King Saud University, Riyadh, Saudi Arabia
- Ibrahim A. Almaghlouth
- 1College of Medicine Research Center, College of Medicine, King Saud University, Riyadh, Saudi Arabia
- Maria Cristina Maggio
- 2University Department of Health Promotion, Mother and Child Care, Internal Medicine and Medical Specialties (PROMISE) "G. D'Alessandro", University of Palermo, Palermo, Italy
- Jurgen Sota
- Department of Medical Sciences, Surgery and Neurosciences, Research Center of Systemic Autoinflammatory Diseases and Behçet's Disease Clinic, University of Siena, Siena, Italy
- Jurgen Sota
- Azienda Ospedaliero-Universitaria Senese, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Siena, Italy
- Abdurrahman Tufan
- 3Department of Internal Medicine, Division of Rheumatology, Gazi University Hospital, Ankara, Türkiye
- Andrea Hinojosa-Azaola
- 4Department of Immunology and Rheumatology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico
- Florenzo Iannone
- Department of Precision and Regenerative Medicine and Ionian Area (DiMePRe-J) Policlinic Hospital, University of Bari, Bari, Italy
- Roberta Loconte
- Department of Pediatrics, Pediatric Rheumatology Center, Giovanni XXIII Pediatric Hospital, University of Bari, Bari, Italy
- Katerina Laskari
- 5Joint Academic Rheumatology Program, The First Department of Propaedeutic and Internal Medicine, School of Medicine, National and Kapodistrian University of Athens, Athens, Greece
- Haner Direskeneli
- 6Department of Internal Medicine, Division of Rheumatology, Marmara University, Faculty of Medicine, Istanbul, Türkiye
- Piero Ruscitti
- 7Rheumatology Unit, Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, L'Aquila, Italy
- Maria Morrone
- Department of Precision and Regenerative Medicine and Ionian Area (DiMePRe-J) Policlinic Hospital, University of Bari, Bari, Italy
- Henrique A. Mayrink Giardini
- 8Rheumatology Division, Faculdade de Medicina, Hospital das Clínicas, Universidade de São Paulo, São Paulo, Brazil
- Alexandros Panagiotopoulos
- Joint Academic Rheumatology Program, Medical School, National and Kapodistrian University of Athens, Athens, Greece
- Ilenia Di Cola
- 7Rheumatology Unit, Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, L'Aquila, Italy
- Eduardo Martín-Nares
- 4Department of Immunology and Rheumatology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico
- Sara Monti
- 9Division of Rheumatology, Fondazione IRCCS Policlinico San Matteo, Pavia, Italy
- Sara Monti
- 0Department of Internal Medicine and Therapeutics, Università di Pavia, Pavia, Italy
- Ludovico De Stefano
- 9Division of Rheumatology, Fondazione IRCCS Policlinico San Matteo, Pavia, Italy
- Ludovico De Stefano
- 0Department of Internal Medicine and Therapeutics, Università di Pavia, Pavia, Italy
- Rıza Can Kardas
- 3Department of Internal Medicine, Division of Rheumatology, Gazi University Hospital, Ankara, Türkiye
- Rahime Duran
- 3Department of Internal Medicine, Division of Rheumatology, Gazi University Hospital, Ankara, Türkiye
- Corrado Campochiaro
- Division of Immunology, Transplants and Infectious Diseases, Università Vita-Salute San Raffaele, Milan, Italy
- Corrado Campochiaro
- Unit of Immunology, Rheumatology, Allergy and Rare Diseases, IRCCS Ospedale San Raffaele, Milan, Italy
- Alessandro Tomelleri
- Division of Immunology, Transplants and Infectious Diseases, Università Vita-Salute San Raffaele, Milan, Italy
- Alessandro Tomelleri
- Unit of Immunology, Rheumatology, Allergy and Rare Diseases, IRCCS Ospedale San Raffaele, Milan, Italy
- Abdulaziz Mohammed Alabdulkareem
- 0Rheumatology Unit, Department of Medicine, College of Medicine, King Saud University, Riyadh, Saudi Arabia
- Carla Gaggiano
- Department of Medical Sciences, Surgery and Neurosciences, Research Center of Systemic Autoinflammatory Diseases and Behçet's Disease Clinic, University of Siena, Siena, Italy
- Carla Gaggiano
- Azienda Ospedaliero-Universitaria Senese, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Siena, Italy
- Maria Tarsia
- 1, Department of Molecular Medicine and DevelopmentClinical Pediatrics, University of Siena, Siena, Italy
- Maria Tarsia
- Azienda Ospedaliero-Universitaria Senese, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Siena, Italy
- Elena Bartoloni
- 2Rheumatology Unit, Department of Medicine and Surgery, University of Perugia, Perugia, Italy
- Mery Romeo
- 3Pediatric Nephrology and Rheumatology Unit, Azienda Ospedaliera Universitaria (AOU), "G. Martino", Messina, Italy
- Mohamed A. Hussein
- Rheumatology and Clinical Immunology Unit, Internal Medicine Department, Faculty of Medicine, Cairo University, Giza, Egypt
- Ahmed Hatem Laymouna
- Rheumatology and Clinical Immunology Unit, Internal Medicine Department, Faculty of Medicine, Cairo University, Giza, Egypt
- Isabele Parente de Brito Antonelli
- 8Rheumatology Division, Faculdade de Medicina, Hospital das Clínicas, Universidade de São Paulo, São Paulo, Brazil
- Marilia Ambiel Dagostin
- 8Rheumatology Division, Faculdade de Medicina, Hospital das Clínicas, Universidade de São Paulo, São Paulo, Brazil
- Lampros Fotis
- 4Department of Pediatrics, Attikon General Hospital, National and Kapodistrian University of Athens, Zografou, Greece
- Sara Bindoli
- 5Rheumatology Unit, Department of Medicine, University of Padua, Padua, Italy
- Luca Navarini
- 6Clinical and Research Section of Rheumatology and Clinical Immunology, Fondazione Policlinico Campus Bio-Medico, Rome, Italy
- Luca Navarini
- 7Rheumatology, Immunology and Clinical Medicine Unit, Department of Medicine, School of Medicine, University of Rome “Campus Biomedico”, Rome, Italy
- Fatma Alibaz-Oner
- 6Department of Internal Medicine, Division of Rheumatology, Marmara University, Faculty of Medicine, Istanbul, Türkiye
- Gizem Sevik
- 6Department of Internal Medicine, Division of Rheumatology, Marmara University, Faculty of Medicine, Istanbul, Türkiye
- Micol Frassi
- 8Spedali Civili and Department of Clinical and Experimental Sciences, Rheumatology and Clinical Immunology, University of Brescia, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Brescia, Italy
- Francesco Ciccia
- 9Department of Precision Medicine, University of Campania "Luigi Vanvitelli", Naples, Italy
- Daniela Iacono
- 9Department of Precision Medicine, University of Campania "Luigi Vanvitelli", Naples, Italy
- Francesca Crisafulli
- 8Spedali Civili and Department of Clinical and Experimental Sciences, Rheumatology and Clinical Immunology, University of Brescia, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Brescia, Italy
- Piero Portincasa
- 0Clinica Medica "A. Murri", Division of Internal Medicine, Department of Precision and Regenerative Medicine and Ionian Area (DiMePre-J), University of Bari Aldo Moro, Bari, Italy
- Nour Jaber
- 0Clinica Medica "A. Murri", Division of Internal Medicine, Department of Precision and Regenerative Medicine and Ionian Area (DiMePre-J), University of Bari Aldo Moro, Bari, Italy
- Perla Ayumi Kawakami-Campos
- 1Department of Ophthalmology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico
- Ewa Wiesik-Szewczyk
- 2Department of Internal Medicine, Pneumonology, Allergology and Clinical Immunology, Central Clinical Hospital of the Ministry of National Defense, Military Institute of Medicine, National Research Institute, Warsaw, Poland
- Annamaria Iagnocco
- 3Academic Rheumatology Centre, Dipartimento Scienze Cliniche e Biologiche, Università degli Studi di Torino, Torino, Italy
- Gabriele Simonini
- 4NEUROFARBA Department, Rheumatology Unit, Meyer Children's Hospital IRCCS, University of Florence, Florence, Italy
- Paolo Sfriso
- 5Rheumatology Unit, Department of Medicine, University of Padua, Padua, Italy
- Alberto Balistreri
- 5Bioengineering and Biomedical Data Science Lab, Department of Medical Biotechnologies, University of Siena, Siena, Italy
- Roberto Giacomelli
- 6Clinical and Research Section of Rheumatology and Clinical Immunology, Fondazione Policlinico Campus Bio-Medico, Rome, Italy
- Roberto Giacomelli
- 7Rheumatology, Immunology and Clinical Medicine Unit, Department of Medicine, School of Medicine, University of Rome “Campus Biomedico”, Rome, Italy
- Giovanni Conti
- 3Pediatric Nephrology and Rheumatology Unit, Azienda Ospedaliera Universitaria (AOU), "G. Martino", Messina, Italy
- Bruno Frediani
- Department of Medical Sciences, Surgery and Neurosciences, Research Center of Systemic Autoinflammatory Diseases and Behçet's Disease Clinic, University of Siena, Siena, Italy
- Bruno Frediani
- Azienda Ospedaliero-Universitaria Senese, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Siena, Italy
- Claudia Fabiani
- 6Ophthalmology Unit, Department of Medicine, Surgery and Neurosciences, University of Siena, Siena, Italy
- Claudia Fabiani
- Azienda Ospedaliero-Universitaria Senese, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Siena, Italy
- Luca Cantarini
- Department of Medical Sciences, Surgery and Neurosciences, Research Center of Systemic Autoinflammatory Diseases and Behçet's Disease Clinic, University of Siena, Siena, Italy
- Luca Cantarini
- Azienda Ospedaliero-Universitaria Senese, European Reference Network (ERN) for Rare Immunodeficiency, Autoinflammatory and Autoimmune Diseases (RITA) Center, Siena, Italy
- DOI
- https://doi.org/10.3389/fmed.2023.1256243
- Journal volume & issue
-
Vol. 10
Abstract
IntroductionThe effectiveness of canakinumab may change according to the different times it is used after Still’s disease onset. This study aimed to investigate whether canakinumab (CAN) shows differences in short- and long-term therapeutic outcomes, according to its use as different lines of biologic treatment.MethodsPatients included in this study were retrospectively enrolled from the AutoInflammatory Disease Alliance (AIDA) International Registry dedicated to Still’s disease. Seventy-seven (51 females and 26 males) patients with Still’s disease were included in the present study. In total, 39 (50.6%) patients underwent CAN as a first-line biologic agent, and the remaining 38 (49.4%) patients were treated with CAN as a second-line biologic agent or subsequent biologic agent.ResultsNo statistically significant differences were found between patients treated with CAN as a first-line biologic agent and those previously treated with other biologic agents in terms of the frequency of complete response (p =0.62), partial response (p =0.61), treatment failure (p >0.99), and frequency of patients discontinuing CAN due to lack or loss of efficacy (p =0.2). Of all the patients, 18 (23.4%) patients experienced disease relapse during canakinumab treatment, 9 patients were treated with canakinumab as a first-line biologic agent, and nine patients were treated with a second-line or subsequent biologic agent. No differences were found in the frequency of glucocorticoid use (p =0.34), daily glucocorticoid dosage (p =0.47), or concomitant methotrexate dosage (p =0.43) at the last assessment during CAN treatment.ConclusionCanakinumab has proved to be effective in patients with Still’s disease, regardless of its line of biologic treatment.
Keywords