Pseudoxanthoma Elasticum With Detailed Analyses of Coronary Artery Disease

Tomohiro Fujisaki, MD; Masanobu Ishii, MD, PhD, MPH; Bengo Atari, MD, PhD; Tomoyo Matsumura, MD, PhD; Kenichi Tsujita, MD, PhD

JACC: Case Reports (Jun 2023)

Pseudoxanthoma Elasticum With Detailed Analyses of Coronary Artery Disease

Tomohiro Fujisaki, MD,
Masanobu Ishii, MD, PhD, MPH,
Bengo Atari, MD, PhD,
Tomoyo Matsumura, MD, PhD,
Kenichi Tsujita, MD, PhD

Affiliations

Tomohiro Fujisaki, MD: Department of Cardiovascular Medicine, Graduate School of Medical Sciences, Kumamoto University, Kumamoto, Japan; Department of Cardiovascular Medicine, National Cerebral and Cardiovascular Center, Osaka, Japan
Masanobu Ishii, MD, PhD, MPH: Department of Cardiovascular Medicine, Graduate School of Medical Sciences, Kumamoto University, Kumamoto, Japan; Address for correspondence: Dr Masanobu Ishii, Department of Cardiovascular Medicine, Graduate School of Medical Sciences, Kumamoto University, 1-1-1 Honjo, Chuo-ku, Kumamoto 860-8556, Japan.
Bengo Atari, MD, PhD: Department of Dermatology, Graduate School of Medical Sciences, Kumamoto University, Kumamoto, Japan
Tomoyo Matsumura, MD, PhD: Department of Ophthalmology, Faculty of Life Sciences, Kumamoto University, Kumamoto, Japan
Kenichi Tsujita, MD, PhD: Department of Cardiovascular Medicine, Graduate School of Medical Sciences, Kumamoto University, Kumamoto, Japan

Journal volume & issue: Vol. 16
p. 101894

Abstract

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A 60-year-old woman with pseudoxanthoma elasticum (PXE) underwent thorough coronary artery disease assessments. Intravascular imaging tests suggested fragmented and calcified elastic fibers in the internal elastic lamina, suggesting a possible pathophysiology of coronary artery disease in PXE. Our case report would allow clinicians to acknowledge the clinical picture of PXE. (Level of Difficulty: Intermediate.)

Published in JACC: Case Reports

ISSN: 2666-0849 (Online)
Publisher: Elsevier
Country of publisher: United States
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Diseases of the circulatory (Cardiovascular) system
Website: https://www.journals.elsevier.com/jacc-case-reports

About the journal

Abstract

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