Oral and Maxillofacial Surgery Cases (Sep 2019)

Three-dimensional treatment planning and treatment protocol in embryonal rhabdomyosarcoma and orthognathic surgery: A case report

  • Sohaib Shujaat,
  • Reinhilde Jacobs,
  • Eman Shaheen,
  • Steven Michiels,
  • Constantinus Politis

Journal volume & issue
Vol. 5, no. 3

Abstract

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Rhabdomyosarcoma (RMS) is one of the most common soft tissue sarcomas encountered in paediatric patients. Embryonal rhabdomyosarcoma (ERMS), a variant of RMS, is observed in more than 70% of the cases and predominantly arises from head and neck region and genitourinary tract of children and young adults. Treatment is dependent on the size, location and extent of the tumor. This case report describes a 10 years old patient who received chemo- and radiotherapy. Three-dimensional (3D) conformal radiation therapy planning was carried out. The patient later suffered from asymmetric facial growth which was corrected with orthognathic surgery following 3D virtual surgical planning. Keywords: Embryonal rhabdomyosarcoma, Orthognathic surgery, Radiotherapy, Chemotherapy